How does Stickler syndrome affect connective tissues, vision, and hearing?

They have more stereocilia and long stereocilia relative to kinocilia heights. Tip link tensions show parallel behavior in peripheral columns of the bundle ... Nov 7, 2011 ... The output of the cochlea is controlled by the bending of inner‐hair‐cell (IHC) stereocilia, but the mechanisms that produce this bending ... ... stereocilia bathing in the surrounding endolymph. The cell body itself is localised in the perilymph compartment (see transverse section of the organ of ... Jun 20, 2019 ... We report that TRIOBP-5 is essential for thickening bundles of F-actin in rootlets, establishing their mature dimensions and for stiffening supporting cells. This article obtains the stereocilia movement generated by basilar membrane (BM) vibration based on the positional relationship between the various structures ... Aug 23, 2016 ... Abstract. Stereocilia are actin-based protrusions on auditory and vestibular sensory cells that are required for hearing and balance. They ... Sep 8, 2022 ... Stereocilia transform audio waves of sound into electrical impulses ... Our cells rely on a healthy supply of blood throughout our body, and this ... Deflection of the bundle of stereocilia is mechanically responsible for stretching ion pores in the stereocilia, allowing a cation current to pass into the cell ... Jul 21, 2022 ... Sensorineural Hearing Loss. Inside the inner ear is the cochlea, which is lined with tiny hair cells called stereocilia that convert soundwaves ... May 24, 2023 ... Stereocilia are vital for the transmission of sound as they house the mechanoelectrical transduction channels triggered by the bending of the ...